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Rabbit Anti-ACAD9 Antibody (CSB-PA887999ESR1HU)
Supplier: CUSABIO BIOTECH CO.
ACAD-9 Antibody,ACAD9 AntibodyMore alternative names for the antibody
Acyl CoA dehydrogenase 9 antibody|Acyl Coenzyme A dehydrogenase family, member 9 antibody|acyl-CoA dehydrogenase family member 9, mitochondrial antibody|FLJ23533 antibody|MGC14452 antibody|NPD002 antibody|Very long chain acyl CoA dehydrogenase VLCAD antibody
Anti-ACAD9 antibody (ab99952)
Anti-ACAD9 antibody (ab99952)
Recommended applications: ELISA, WB, IHC
Recommended dilution: Recommended dilution:WB:1:200-1000,IHC:1:20-1:200
Recommended protocols: check protocols
|Catalogue No.|| |
Recombinant human Acyl-CoA dehydrogenase family member 9, mitochondrial protein (1-270AA)
ELISA, WB, IHC
|Recommended dilution|| |
|Molecular weight|| |
Antigen Affinity Purified
Shipped at 4 Celcius Degree. Upon delivery aliquot and store at -20 Celcius Degree or -80 Celcius Degree. Avoid repeated freeze.
|Database links|| |
<a href="http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=gene&cmd=Retrieve&dopt=Graphics&list_uids=28976" target="_blank">Entrez Gene:28976( Human)</a>, <a href="http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=gene&cmd=Retrieve&dopt=Graphics&list_uids=229211" target="_blank">Entrez Gene:229211( Mouse)</a>, <a href="http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=gene&cmd=Retrieve&dopt=Graphics&list_uids=294973" target="_blank">Entrez Gene:294973( Rat)</a>, <a href="http://www.ncbi.nlm.nih.gov/omim/611103" target="_blank">Omim:611103( Human)</a>, <a href="http://www.uniprot.org/uniprot/Q9H845" target="_blank">SwissProt:Q9H845( Human)</a>, <a href="http://www.uniprot.org/uniprot/Q8JZN5" target="_blank">SwissProt:Q8JZN5( Mouse)</a>, <a href="http://www.ncbi.nlm.nih.gov/UniGene/clust.cgi?ORG=Hs&CID=567482" target="_blank">Unigene:567482( Human)</a>
|Protein function|| |
Required for mitochondrial complex I assembly (PubMed:20816094, PubMed:24158852). Has a dehydrogenase activity on palmitoyl-CoA (C16:0) and stearoyl-CoA (C18:0). It is three times more active on palmitoyl-CoA than on stearoyl-CoA. However, it does not play a primary role in long-chain fatty acid oxidation in vivo (PubMed:20816094, PubMed:24158852). Has little activity on octanoyl-CoA (C8:0), butyryl-CoA (C4:0) or isovaleryl-CoA (5:0). .
|Protein tissue specificity|| |
Ubiquitously expressed in most normal human tissues and cancer cell lines with high level of expression in heart, skeletal muscles, brain, kidney and liver. .
|Involvement in disease|| |
Acyl-CoA dehydrogenase family, member 9, deficiency (ACAD9 deficiency) [MIM:611126]: An autosomal recessive metabolic disorder associated with mitochondrial complex I deficiency, resulting in multisystemic and variable manifestations. Clinical features include infantile onset of acute metabolic acidosis, Reye-like episodes (brain edema and vomiting that may rapidly progress to seizures, coma and death), exercise intolerance, hypertrophic cardiomyopathy, liver failure, muscle weakness, and neurologic dysfunction. . Note=The disease is caused by mutations affecting the gene represented in this entry.
|Protein sequence and domain|| |
Belongs to the acyl-CoA dehydrogenase family.
|Protein cellular localization|| |
|Research area|| |
<a href="https://antibodyplus.com/research-areas/">All research areas</a>><a href="https://antibodyplus.com/Synthesis-and-Degradation/">Synthesis and Degradation</a>><a href="https://antibodyplus.com/product-tag/ACAD/">ACAD</a><br><a href="https://antibodyplus.com/product-tag/Synthesis-and-Degradation/"> (View all antibody categories related to Synthesis and Degradation)</a>
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CUSABIO BIOTECH CO.
|Product type|| |
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