Anti-ACAD9 Antibody

$99.00$319.00

Reactivity: Human
Applications: ELISA,WB,IHC
Conjugation: Various
Supplier: CUSABIO BIOTECH CO.

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Rabbit Anti-ACAD9 Antibody (CSB-PA887999ESR1HU)

Supplier: CUSABIO BIOTECH CO.

Alternative names:

ACAD-9 Antibody,ACAD9 Antibody

More alternative names for the antibody
Acyl CoA dehydrogenase 9 antibody|Acyl Coenzyme A dehydrogenase family, member 9 antibody|acyl-CoA dehydrogenase family member 9, mitochondrial antibody|FLJ23533 antibody|MGC14452 antibody|NPD002 antibody|Very long chain acyl CoA dehydrogenase VLCAD antibody
Anti-ACAD9 antibody (ab99952)
Close sc-135148|

Recommended applications: ELISA, WB, IHC

Recommended dilution: Recommended dilution:WB:1:200-1000,IHC:1:20-1:200

Recommended protocols: check protocols

Name

Anti-ACAD9 Antibody

Catalogue No.

CSB-PA887999ESR1HU

Reactivity

Human

Immunogen

Recombinant human Acyl-CoA dehydrogenase family member 9, mitochondrial protein (1-270AA)

Host

Rabbit

Applications

ELISA, WB, IHC

Recommended dilution

Recommended dilution:WB:1:200-1000,IHC:1:20-1:200

Clonality

Polyclonal

Conjugation

unconjugated

Isotype

IgG

Molecular weight

68 kDa

Purification

Antigen Affinity Purified

Storage

Shipped at 4 Celcius Degree. Upon delivery aliquot and store at -20 Celcius Degree or -80 Celcius Degree. Avoid repeated freeze.

Database links

Entrez Gene:28976( Human), Entrez Gene:229211( Mouse), Entrez Gene:294973( Rat), Omim:611103( Human), SwissProt:Q9H845( Human), SwissProt:Q8JZN5( Mouse), Unigene:567482( Human)

Protein function

Required for mitochondrial complex I assembly (PubMed:20816094, PubMed:24158852). Has a dehydrogenase activity on palmitoyl-CoA (C16:0) and stearoyl-CoA (C18:0). It is three times more active on palmitoyl-CoA than on stearoyl-CoA. However, it does not play a primary role in long-chain fatty acid oxidation in vivo (PubMed:20816094, PubMed:24158852). Has little activity on octanoyl-CoA (C8:0), butyryl-CoA (C4:0) or isovaleryl-CoA (5:0). .

Protein tissue specificity

Ubiquitously expressed in most normal human tissues and cancer cell lines with high level of expression in heart, skeletal muscles, brain, kidney and liver. .

Involvement in disease

Acyl-CoA dehydrogenase family, member 9, deficiency (ACAD9 deficiency) [MIM:611126]: An autosomal recessive metabolic disorder associated with mitochondrial complex I deficiency, resulting in multisystemic and variable manifestations. Clinical features include infantile onset of acute metabolic acidosis, Reye-like episodes (brain edema and vomiting that may rapidly progress to seizures, coma and death), exercise intolerance, hypertrophic cardiomyopathy, liver failure, muscle weakness, and neurologic dysfunction. . Note=The disease is caused by mutations affecting the gene represented in this entry.

Protein sequence and domain

Belongs to the acyl-CoA dehydrogenase family.

Protein cellular localization

Mitochondrion .

Research area

All research areas>Synthesis and Degradation>ACAD
(View all antibody categories related to Synthesis and Degradation)

Note

AntibodyPlus provides antibody trial sample for your own antibody validation and collects antibody reviews.

Supplier

CUSABIO BIOTECH CO.

Product type

Primary antibody

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