Anti-ALG2 Antibody

$99.00$319.00

Reactivity: Human
Applications: ELISA,IHC
Conjugation: Various
Supplier: CUSABIO BIOTECH CO.

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Rabbit Anti-ALG2 Antibody (CSB-PA863983ESR1HU)

Supplier: CUSABIO BIOTECH CO.

Alternative names:

Alpha-1 Antibody,3/1 Antibody,6-mannosyltransferase ALG2 Antibody,Asparagine-linked glycosylation protein 2 homolog Antibody,GDP-Man:Man(1)GlcNAc(2)-PP-Dol alpha-1 Antibody,3-mannosyltransferase Antibody,GDP-Man:Man(1)GlcNAc(2)-PP-dolichol mannosyltransferase Antibody,GDP-Man:Man(2)GlcNAc(2)-PP-Dol alpha-1 Antibody,6-mannosyltransferase Antibody,ALG2 Antibody,UNQ666/PRO1298 Antibody

More alternative names for the antibody
3-mannosyltransferase ALG2 antibody|ALG2 alpha-1,3/1,6-mannosyltransferase antibody|ALG2 antibody|ALG2_HUMAN antibody|Alpha 1,3 mannosyltransferase ALG2 antibody|Alpha-1 antibody|Asparagine linked glycosylation protein 2 antibody|Asparagine-linked glycosylation protein 2 homolog antibody|CDGIi antibody|FLJ14511 antibody|GDP Man:Man(1)GlcNAc(2) PP dolichol mannosyltransferase antibody|GDP-Man:Man(1)GlcNAc(2)-PP-dolichol mannosyltransferase antibody|hALPG2 antibody|NET38 antibody|OTTHUMP00000021785 antibody|OTTHUMP00000123474 antibody|RP11-13B9.1 antibody
Anti-ALG2 antibody [EPR12007(2)(B)] (ab181124)
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Recommended applications: ELISA, IHC

Recommended dilution: Recommended dilution:IHC:1:20-1:200

Recommended protocols: check protocols

Name

Anti-ALG2 Antibody

Catalogue No.

CSB-PA863983ESR1HU

Reactivity

Human

Immunogen

Recombinant human Alpha-1,3/1,6-mannosyltransferase ALG2 protein (197-416AA)

Host

Rabbit

Applications

ELISA, IHC

Recommended dilution

Recommended dilution:IHC:1:20-1:200

Clonality

Polyclonal

Conjugation

unconjugated

Isotype

IgG

Molecular weight

47 kDa

Purification

Antigen Affinity Purified

Storage

Shipped at 4 Celcius Degree. Upon delivery aliquot and store at -20 Celcius Degree or -80 Celcius Degree. Avoid repeated freeze.

Database links

Entrez Gene:85365( Human), Omim:607905( Human), SwissProt:Q9H553( Human), Unigene:40919( Human)

Protein function

Mannosylates Man(2)GlcNAc(2)-dolichol diphosphate and Man(1)GlcNAc(2)-dolichol diphosphate to form Man(3)GlcNAc(2)-dolichol diphosphate. .

Involvement in disease

Congenital disorder of glycosylation 1I (CDG1I) [MIM:607906]: A form of congenital disorder of glycosylation, a multisystem disorder caused by a defect in glycoprotein biosynthesis and characterized by under-glycosylated serum glycoproteins. Congenital disorders of glycosylation result in a wide variety of clinical features, such as defects in the nervous system development, psychomotor retardation, dysmorphic features, hypotonia, coagulation disorders, and immunodeficiency. The broad spectrum of features reflects the critical role of N-glycoproteins during embryonic development, differentiation, and maintenance of cell functions. . Note=The disease is caused by mutations affecting the gene represented in this entry.; Myasthenic syndrome, congenital, 14 (CMS14) [MIM:616228]: A form of congenital myasthenic syndrome, a group of disorders characterized by failure of neuromuscular transmission, including pre-synaptic, synaptic, and post-synaptic disorders that are not of autoimmune origin. Clinical features are easy fatigability and muscle weakness. CMS14 is an autosomal recessive form characterized by onset of limb-girdle muscle weakness in early childhood. The disorder is slowly progressive, and some patients may become wheelchair-bound. . Note=The disease is caused by mutations affecting the gene represented in this entry.

Protein sequence and domain

Belongs to the glycosyltransferase group 1 family. Glycosyltransferase 4 subfamily.

Protein cellular localization

Membrane ; Single-pass membrane protein .

Note

AntibodyPlus provides antibody trial sample for your own antibody validation and collects antibody reviews.

Supplier

CUSABIO BIOTECH CO.

Product type

Primary antibody

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