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Rabbit Anti-GATM Antibody (CSB-PA009284ESR1HU)
Supplier: CUSABIO BIOTECH CO.
L-arginine:glycine amidinotransferase Antibody,Transamidinase Antibody,GATM Antibody,AGAT AntibodyMore alternative names for the antibody
AGAT antibody|AT antibody|GATM antibody|GATM_HUMAN antibody|Glycine amidinotransferase antibody|Glycine amidinotransferase, mitochondrial antibody|L-arginine:glycine amidinotransferase antibody|mitochondrial antibody|Transamidinase antibody
Anti-GATM antibody (ab87062)
Anti-GATM antibody (ab87062)
Recommended applications: ELISA, WB, IHC
Recommended dilution: Recommended dilution:WB:1:500-5000,IHC:1:20-1:200
Recommended protocols: check protocols
|Catalogue No.|| |
Recombinant human Glycine amidinotransferase, mitochondrial protein (124-423AA)
ELISA, WB, IHC
|Recommended dilution|| |
|Molecular weight|| |
Antigen Affinity Purified
Shipped at 4 Celcius Degree. Upon delivery aliquot and store at -20 Celcius Degree or -80 Celcius Degree. Avoid repeated freeze.
|Database links|| |
Entrez Gene:2628( Human), Entrez Gene:67092( Mouse), Entrez Gene:81660( Rat), Entrez Gene:266799( Zebrafish), Omim:602360( Human), SwissProt:P50440( Human), SwissProt:Q9D964( Mouse), SwissProt:P50442( Rat), SwissProt:Q6PH19( Zebrafish), Unigene:75335( Human), Unigene:29975( Mouse), Unigene:17661( Rat), Unigene:75520( Zebrafish)
|Protein function|| |
Catalyzes the biosynthesis of guanidinoacetate, the immediate precursor of creatine. Creatine plays a vital role in energy metabolism in muscle tissues. May play a role in embryonic and central nervous system development. May be involved in the response to heart failure by elevating local creatine synthesis. .
|Protein tissue specificity|| |
Expressed in brain, heart, kidney, liver, lung, salivary gland and skeletal muscle tissue, with the highest expression in kidney. Biallelically expressed in placenta and fetal tissues. .
|Involvement in disease|| |
Cerebral creatine deficiency syndrome 3 (CCDS3) [MIM:612718]: An autosomal recessive disorder characterized by developmental delay/regression, mental retardation, severe disturbance of expressive and cognitive speech, and severe depletion of creatine/phosphocreatine in the brain. Most patients develop a myopathy characterized by muscle weakness and atrophy later in life. . Note=The disease is caused by mutations affecting the gene represented in this entry.
|Protein sequence and domain|| |
Belongs to the amidinotransferase family. One chain folds into a compact single domain composed of repeating units, five beta-beta-alpha-beta modules, which surround the central active site.
|Protein cellular localization|| |
Isoform 1: Mitochondrion inner membrane; Peripheral membrane protein; Intermembrane side. Note=Probably attached to the outer side of the inner membrane.; Isoform 2: Cytoplasm.
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CUSABIO BIOTECH CO.
|Product type|| |
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