Anti-GUSB Antibody

$99.00$319.00

Reactivity: Human
Applications: ELISA,IHC
Conjugation: Various
Supplier: CUSABIO BIOTECH CO.

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Rabbit Anti-GUSB Antibody (CSB-PA010064ESR1HU)

Supplier: CUSABIO BIOTECH CO.

Alternative names:

Beta-G1 Antibody,GUSB Antibody

More alternative names for the antibody
Ac2-223 antibody|asd antibody|Beta G1 antibody|Beta glucuronidase antibody|Beta-G1 antibody|Beta-glucuronidase antibody|BG antibody|BGLR antibody|BGLR_HUMAN antibody|FLJ39445 antibody|Glucuronidase beta antibody|Gur antibody|Gus antibody|Gus-r antibody|Gus-s antibody|Gus-t antibody|Gus-u antibody|GUSB antibody|Gut antibody|MPS7 antibody
Anti-beta glucuronidase (GUSB) antibody [EPR10616] (ab166904)
Close sc-26283|sc-374629|sc-25827|sc-26282|

Recommended applications: ELISA, IHC

Recommended dilution: Recommended dilution:IHC:1:20-1:200

Recommended protocols: check protocols

Name

Anti-GUSB Antibody

Catalogue No.

CSB-PA010064ESR1HU

Reactivity

Human

Immunogen

Recombinant human Beta-glucuronidase protein (382-651AA)

Host

Rabbit

Applications

ELISA, IHC

Recommended dilution

Recommended dilution:IHC:1:20-1:200

Clonality

Polyclonal

Conjugation

unconjugated

Isotype

IgG

Molecular weight

74 kDa

Purification

Antigen Affinity Purified

Storage

Shipped at 4 Celcius Degree. Upon delivery aliquot and store at -20 Celcius Degree or -80 Celcius Degree. Avoid repeated freeze.

Database links

Entrez Gene:2990( Human), Omim:611499( Human), SwissProt:P08236( Human), Unigene:255230( Human)

Protein function

Plays an important role in the degradation of dermatan and keratan sulfates.

Involvement in disease

Mucopolysaccharidosis 7 (MPS7) [MIM:253220]: An autosomal recessive lysosomal storage disease characterized by inability to degrade glucuronic acid-containing glycosaminoglycans. The phenotype is highly variable, ranging from severe lethal hydrops fetalis to mild forms with survival into adulthood. Most patients with the intermediate phenotype show hepatomegaly, skeletal anomalies, coarse facies, and variable degrees of mental impairment. . Note=The disease is caused by mutations affecting the gene represented in this entry.

Protein sequence and domain

Belongs to the glycosyl hydrolase 2 family.

Protein post-translational modifications

N-linked glycosylated with 3 to 4 oligosaccharide chains. .

Protein cellular localization

Lysosome.

Research area

All research areas>Synthesis and Degradation>β-glucuronidase
(View all antibody categories related to Synthesis and Degradation)

Note

AntibodyPlus provides antibody trial sample for your own antibody validation and collects antibody reviews.

Supplier

CUSABIO BIOTECH CO.

Product type

Primary antibody

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