Anti-L2HGDH Antibody

$99.00$319.00

Reactivity: Human,Mouse
Applications: ELISA,WB,IHC
Conjugation: Various
Supplier: CUSABIO BIOTECH CO.

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Rabbit Anti-L2HGDH Antibody (CSB-PA864008ESR2HU)

Supplier: CUSABIO BIOTECH CO.

Alternative names:

L-2-hydroxyglutarate dehydrogenase Antibody,mitochondrial Antibody,Duranin Antibody,L2HGDH Antibody,C14orf160 Antibody

More alternative names for the antibody
2 hydroxyglutarate dehydrogenase antibody|Alpha hydroxyglutarate oxidoreductase antibody|Alpha ketoglutarate reductase antibody|C14orf160 antibody|Duranin antibody|FLJ12618 antibody|L alpha hydroxyglutarate dehydrogenase antibody|L-2-hydroxyglutarate dehydrogenase antibody|L-2-hydroxyglutarate dehydrogenase, mitochondrial antibody|L2HDH_HUMAN antibody|l2hgdh antibody|mitochondrial antibody
Anti-L2HGDH antibody (ab108012)
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Recommended applications: ELISA, WB, IHC

Recommended dilution: User optimized

Recommended protocols: check protocols

Name

Anti-L2HGDH Antibody

Catalogue No.

CSB-PA864008ESR2HU

Reactivity

Human, Mouse

Immunogen

Recombinant human L-2-hydroxyglutarate dehydrogenase, mitochondrial protein (1-220AA)

Host

Rabbit

Applications

ELISA, WB, IHC

Recommended dilution

User optimized

Clonality

Polyclonal

Conjugation

unconjugated

Isotype

IgG

Molecular weight

50 kDa

Purification

Antigen Affinity Purified

Storage

Shipped at 4 Celcius Degree. Upon delivery aliquot and store at -20 Celcius Degree or -80 Celcius Degree. Avoid repeated freeze.

Database links

Entrez Gene:79944( Human), Entrez Gene:217666( Mouse), Omim:609584( Human), SwissProt:Q9H9P8( Human), SwissProt:Q91YP0( Mouse), Unigene:256034( Human), Unigene:103362( Mouse)

Protein tissue specificity

Widely expressed. Highly expressed in brain, testis and muscle. Expressed to a lower extent in lymphocytes, fibroblasts, keratinocytes, placenta, bladder, small intestine, liver and bone marrow. .

Involvement in disease

L-2-hydroxyglutaric aciduria (L2HGA) [MIM:236792]: A rare autosomal recessive disorder clinically characterized by mild psychomotor delay in the first years of life, followed by progressive cerebellar ataxia, dysarthria and moderate to severe mental retardation. Diagnosis is based on the presence of an excess of L-2-hydroxyglutaric acid in urine, blood and cerebrospinal fluid. . Note=The disease is caused by mutations affecting the gene represented in this entry.

Protein sequence and domain

Belongs to the L2HGDH family.

Protein cellular localization

Mitochondrion .

Note

AntibodyPlus provides antibody trial sample for your own antibody validation and collects antibody reviews.

Supplier

CUSABIO BIOTECH CO.

Product type

Primary antibody

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