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Rabbit Anti-NDUFV1 Antibody (CSB-PA015668ESR2HU)
Supplier: CUSABIO BIOTECH CO.
NADH dehydrogenase [ubiquinone] flavoprotein 1 Antibody,mitochondrial Antibody,Complex I-51kD Antibody,CI-51kD Antibody,NADH dehydrogenase flavoprotein 1 Antibody,NADH-ubiquinone oxidoreductase 51 kDa subunit Antibody,NDUFV1 Antibody,UQOR1 AntibodyMore alternative names for the antibody
CI 51kD antibody|CI-51kD antibody|Complex I 51kD antibody|Complex I-51kD antibody|FLJ59059 antibody|mitochondrial antibody|NADH dehydrogenase (ubiquinone) flavoprotein 1 antibody|NADH dehydrogenase [ubiquinone] flavoprotein 1 antibody|NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial antibody|NADH dehydrogenase flavoprotein 1 antibody|NADH ubiquinone oxidoreductase 51 kDa subunit antibody|NADH ubiquinone oxidoreductase antibody|NADH-ubiquinone oxidoreductase 51 kDa subunit antibody|NDUFV 1 antibody|ndufv1 antibody|NDUV1_HUMAN antibody|UQOR1 antibody
Anti-NDUFV1 antibody (ab203208)
Anti-NDUFV1 antibody (ab203208)
Recommended applications: ELISA, WB, IHC
Recommended dilution: User optimized
Recommended protocols: check protocols
|Catalogue No.|| |
Recombinant human NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial protein (1-250AA)
ELISA, WB, IHC
|Recommended dilution|| |
|Molecular weight|| |
Antigen Affinity Purified
Shipped at 4 Celcius Degree. Upon delivery aliquot and store at -20 Celcius Degree or -80 Celcius Degree. Avoid repeated freeze.
|Database links|| |
Entrez Gene:4723( Human), Entrez Gene:17995( Mouse), Entrez Gene:293655( Rat), Omim:161015( Human), SwissProt:P49821( Human), SwissProt:Q91YT0( Mouse), Unigene:7744( Human), Unigene:29842( Mouse), Unigene:3159( Rat)
|Protein function|| |
Core subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I) that is believed to belong to the minimal assembly required for catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone (By similarity). .
|Involvement in disease|| |
Leigh syndrome (LS) [MIM:256000]: An early-onset progressive neurodegenerative disorder characterized by the presence of focal, bilateral lesions in one or more areas of the central nervous system including the brainstem, thalamus, basal ganglia, cerebellum and spinal cord. Clinical features depend on which areas of the central nervous system are involved and include subacute onset of psychomotor retardation, hypotonia, ataxia, weakness, vision loss, eye movement abnormalities, seizures, and dysphagia. . Note=The disease is caused by mutations affecting the gene represented in this entry.; Mitochondrial complex I deficiency (MT-C1D) [MIM:252010]: A disorder of the mitochondrial respiratory chain that causes a wide range of clinical manifestations from lethal neonatal disease to adult-onset neurodegenerative disorders. Phenotypes include macrocephaly with progressive leukodystrophy, non-specific encephalopathy, cardiomyopathy, myopathy, liver disease, Leigh syndrome, Leber hereditary optic neuropathy, and some forms of Parkinson disease. . Note=The disease is caused by mutations affecting the gene represented in this entry.
|Protein sequence and domain|| |
Belongs to the complex I 51 kDa subunit family.
|Protein cellular localization|| |
Mitochondrion inner membrane; Peripheral membrane protein; Matrix side.
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|Product type|| |
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