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Rabbit Anti-PEX7 Antibody (CSB-PA017808ESR2HU)
Supplier: CUSABIO BIOTECH CO.
Peroxisomal targeting signal 2 receptor Antibody,PTS2 receptor Antibody,Peroxin-7 Antibody,PEX7 Antibody,PTS2R AntibodyMore alternative names for the antibody
PBD9B antibody|PCDP1 antibody|Peroxin 7 antibody|Peroxin-7 antibody|Peroxisomal PTS2 receptor antibody|Peroxisomal targeting signal 2 receptor antibody|Peroxisome biogenesis factor 7 antibody|Peroxisome targeting signal 2 receptor antibody|PEX7 antibody|PEX7 protein antibody|PEX7_HUMAN antibody|PTS2 receptor antibody|PTS2R antibody|RCDP1 antibody|RD antibody
Anti-PEX7 antibody (ab92779)
Anti-PEX7 antibody (ab92779)
Recommended applications: ELISA, IHC
Recommended dilution: Recommended dilution:IHC:1:20-1:200
Recommended protocols: check protocols
|Catalogue No.|| |
Recombinant human Peroxisomal targeting signal 2 receptor protein (1-240AA)
|Recommended dilution|| |
|Molecular weight|| |
Antigen Affinity Purified
Shipped at 4 Celcius Degree. Upon delivery aliquot and store at -20 Celcius Degree or -80 Celcius Degree. Avoid repeated freeze.
|Protein function|| |
Binds to the N-terminal PTS2-type peroxisomal targeting signal and plays an essential role in peroxisomal protein import.
|Protein tissue specificity|| |
Ubiquitous. Highest expression in pancreas, skeletal muscle and heart.
|Involvement in disease|| |
Peroxisome biogenesis disorder complementation group 11 (PBD-CG11) [MIM:614879]: A peroxisomal disorder arising from a failure of protein import into the peroxisomal membrane or matrix. The peroxisome biogenesis disorders (PBD group) are genetically heterogeneous with at least 14 distinct genetic groups as concluded from complementation studies. Include disorders are: Zellweger syndrome (ZWS), neonatal adrenoleukodystrophy (NALD), infantile Refsum disease (IRD), and classical rhizomelic chondrodysplasia punctata (RCDP). ZWS, NALD and IRD are distinct from RCDP and constitute a clinical continuum of overlapping phenotypes known as the Zellweger spectrum (PBD-ZSS). Note=The disease is caused by mutations affecting the gene represented in this entry.; Rhizomelic chondrodysplasia punctata 1 (RCDP1) [MIM:215100]: A peroxisome biogenesis disorder. It is characterized by severely disturbed endochondral bone formation, rhizomelic shortening of femur and humerus, vertebral disorders, dwarfism, cataract, cutaneous lesions, facial dysmorphism, and severe mental retardation with spasticity. . Note=The disease is caused by mutations affecting the gene represented in this entry.; Peroxisome biogenesis disorder 9B (PBD9B) [MIM:614879]: A peroxisome biogenesis disorder with unusually mild clinical and biochemical manifestations. Affected individuals manifest a variable phenotype similar to, and in some cases indistinguishable from, classic Refsum disease. Variable features include ocular abnormalities, sensorimotor neuropathy, ichthyosis, deafness, chondrodysplasia punctata without rhizomelia or growth failure. . Note=The disease is caused by mutations affecting the gene represented in this entry.
|Protein sequence and domain|| |
Belongs to the WD repeat peroxin-7 family.
|Protein cellular localization|| |
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CUSABIO BIOTECH CO.
|Product type|| |
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