Anti-PEX7 Antibody

$99.00$319.00

Reactivity: Human
Applications: ELISA,IHC
Conjugation: Various
Supplier: CUSABIO BIOTECH CO.

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Rabbit Anti-PEX7 Antibody (CSB-PA017808ESR2HU)

Supplier: CUSABIO BIOTECH CO.

Alternative names:

Peroxisomal targeting signal 2 receptor Antibody,PTS2 receptor Antibody,Peroxin-7 Antibody,PEX7 Antibody,PTS2R Antibody

More alternative names for the antibody
PBD9B antibody|PCDP1 antibody|Peroxin 7 antibody|Peroxin-7 antibody|Peroxisomal PTS2 receptor antibody|Peroxisomal targeting signal 2 receptor antibody|Peroxisome biogenesis factor 7 antibody|Peroxisome targeting signal 2 receptor antibody|PEX7 antibody|PEX7 protein antibody|PEX7_HUMAN antibody|PTS2 receptor antibody|PTS2R antibody|RCDP1 antibody|RD antibody
Anti-PEX7 antibody (ab92779)
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Recommended applications: ELISA, IHC

Recommended dilution: Recommended dilution:IHC:1:20-1:200

Recommended protocols: check protocols

Name

Anti-PEX7 Antibody

Catalogue No.

CSB-PA017808ESR2HU

Reactivity

Human

Immunogen

Recombinant human Peroxisomal targeting signal 2 receptor protein (1-240AA)

Host

Rabbit

Applications

ELISA, IHC

Recommended dilution

Recommended dilution:IHC:1:20-1:200

Clonality

Polyclonal

Conjugation

unconjugated

Isotype

IgG

Molecular weight

35 kDa

Purification

Antigen Affinity Purified

Storage

Shipped at 4 Celcius Degree. Upon delivery aliquot and store at -20 Celcius Degree or -80 Celcius Degree. Avoid repeated freeze.

Database links

Entrez Gene:5191( Human), Entrez Gene:18634( Mouse), Entrez Gene:308718( Rat), Omim:601757( Human), SwissProt:O00628( Human), SwissProt:P97865( Mouse), Unigene:280932( Human), Unigene:338363( Mouse)

Protein function

Binds to the N-terminal PTS2-type peroxisomal targeting signal and plays an essential role in peroxisomal protein import.

Protein tissue specificity

Ubiquitous. Highest expression in pancreas, skeletal muscle and heart.

Involvement in disease

Peroxisome biogenesis disorder complementation group 11 (PBD-CG11) [MIM:614879]: A peroxisomal disorder arising from a failure of protein import into the peroxisomal membrane or matrix. The peroxisome biogenesis disorders (PBD group) are genetically heterogeneous with at least 14 distinct genetic groups as concluded from complementation studies. Include disorders are: Zellweger syndrome (ZWS), neonatal adrenoleukodystrophy (NALD), infantile Refsum disease (IRD), and classical rhizomelic chondrodysplasia punctata (RCDP). ZWS, NALD and IRD are distinct from RCDP and constitute a clinical continuum of overlapping phenotypes known as the Zellweger spectrum (PBD-ZSS). Note=The disease is caused by mutations affecting the gene represented in this entry.; Rhizomelic chondrodysplasia punctata 1 (RCDP1) [MIM:215100]: A peroxisome biogenesis disorder. It is characterized by severely disturbed endochondral bone formation, rhizomelic shortening of femur and humerus, vertebral disorders, dwarfism, cataract, cutaneous lesions, facial dysmorphism, and severe mental retardation with spasticity. . Note=The disease is caused by mutations affecting the gene represented in this entry.; Peroxisome biogenesis disorder 9B (PBD9B) [MIM:614879]: A peroxisome biogenesis disorder with unusually mild clinical and biochemical manifestations. Affected individuals manifest a variable phenotype similar to, and in some cases indistinguishable from, classic Refsum disease. Variable features include ocular abnormalities, sensorimotor neuropathy, ichthyosis, deafness, chondrodysplasia punctata without rhizomelia or growth failure. . Note=The disease is caused by mutations affecting the gene represented in this entry.

Protein sequence and domain

Belongs to the WD repeat peroxin-7 family.

Protein cellular localization

Peroxisome. Cytoplasm.

Note

AntibodyPlus provides antibody trial sample for your own antibody validation and collects antibody reviews.

Supplier

CUSABIO BIOTECH CO.

Product type

Primary antibody

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