Anti-PHYH Antibody

$99.00$319.00

Reactivity: Human,Mouse
Applications: ELISA,WB,IHC
Conjugation: Various
Supplier: CUSABIO BIOTECH CO.

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Rabbit Anti-PHYH Antibody (CSB-PA017946DSR2HU)

Supplier: CUSABIO BIOTECH CO.

Alternative names:

Phytanic acid oxidase Antibody,Phytanoyl-CoA alpha-hydroxylase Antibody, PhyH Antibody,PHYH Antibody,PAHX Antibody

More alternative names for the antibody
LN1 antibody|LNAP1 antibody|LNAP1, mouse, homolog of antibody|OTTHUMP00000019131 antibody|OTTHUMP00000019132 antibody|OTTHUMP00000179083 antibody|OTTHUMP00000216226 antibody|PAHX antibody|PAHX_HUMAN antibody|peroxisomal antibody|PhyH antibody|PHYH1 antibody|Phytanic acid oxidase antibody|phytanoil-CoA alpha hydroxylase antibody|phytanoyl CoA 2 hydroxylase antibody|Phytanoyl CoA 2 oxoglutarate dioxygenase antibody|Phytanoyl CoA alpha hydroxylase antibody|Phytanoyl CoA dioxygenase antibody|Phytanoyl CoA dioxygenase peroxisomal antibody|Phytanoyl-CoA alpha-hydroxylase antibody|Phytanoyl-CoA dioxygenase antibody|RD antibody
Anti-PHYH antibody (HRP) [S210-5] Close sc-376727|

Recommended applications: ELISA, WB, IHC

Recommended dilution: Recommended dilution:WB:1:200-1000,IHC:1:20-1:200

Recommended protocols: check protocols

Name

Anti-PHYH Antibody

Catalogue No.

CSB-PA017946DSR2HU

Reactivity

Human, Mouse

Immunogen

Recombinant human Phytanoyl-CoA dioxygenase, peroxisomal protein (1-338AA)

Host

Rabbit

Applications

ELISA, WB, IHC

Recommended dilution

Recommended dilution:WB:1:200-1000,IHC:1:20-1:200

Clonality

Polyclonal

Conjugation

unconjugated

Isotype

IgG

Molecular weight

38 kDa

Purification

Antigen Affinity Purified

Storage

Shipped at 4 Celcius Degree. Upon delivery aliquot and store at -20 Celcius Degree or -80 Celcius Degree. Avoid repeated freeze.

Database links

Entrez Gene:5264( Human), Entrez Gene:16922( Mouse), Entrez Gene:114209( Rat), Omim:602026( Human), SwissProt:O14832( Human), SwissProt:O35386( Mouse), SwissProt:P57093( Rat), Unigene:498732( Human), Unigene:391704( Mouse), Unigene:7279( Rat)

Protein function

Converts phytanoyl-CoA to 2-hydroxyphytanoyl-CoA.

Protein tissue specificity

Expressed in liver, kidney, and T-cells, but not in spleen, brain, heart, lung and skeletal muscle.

Involvement in disease

Refsum disease (RD) [MIM:266500]: A rare autosomal recessive peroxisomal disorder characterized by the accumulation of the branched-chain fatty acid, phytanic acid, in blood and tissues. Cardinal clinical features are retinitis pigmentosa, peripheral neuropathy, cerebellar ataxia, and elevated protein levels in the cerebrospinal fluid (CSF). Half of all patients exhibit generalized, mild to moderate ichthyosis resembling ichthyosis vulgaris. Less constant features are nerve deafness, anosmia, skeletal abnormalities, cataracts and cardiac impairment. . Note=The disease is caused by mutations affecting the gene represented in this entry.

Protein sequence and domain

Belongs to the PhyH family.

Protein cellular localization

Peroxisome.

Research area

All research areas>Synthesis and Degradation>PHYH
(View all antibody categories related to Synthesis and Degradation)

Note

AntibodyPlus provides antibody trial sample for your own antibody validation and collects antibody reviews.

Supplier

CUSABIO BIOTECH CO.

Product type

Primary antibody

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