Anti-SGSH Antibody

$99.00$319.00

Reactivity: Human
Applications: ELISA,IHC
Conjugation: Various
Supplier: CUSABIO BIOTECH CO.

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Rabbit Anti-SGSH Antibody (CSB-PA021200ESR1HU)

Supplier: CUSABIO BIOTECH CO.

Alternative names:

Sulfoglucosamine sulfamidase;Sulphamidase;SGSH;HSS Antibody

More alternative names for the antibody
Heparan sulfate sulfatase antibody|Heparan sulphate sulphatase antibody|HSS antibody|MPS 3A antibody|MPS3 A antibody|MPS3A antibody|Mucopolysaccharidosis type IIIA antibody|N sulfoglucosamine sulfohydrolase (sulfamidase) antibody|N sulfoglucosamine sulfohydrolase antibody|N-sulphoglucosamine sulphohydrolase antibody|SFMD antibody|SGSH antibody|SPHM_HUMAN antibody|Sulfoglucosamine sulfamidase antibody|Sulphamidase antibody|Sulphoglucosamine sulphamidase antibody
Anti-SGSH antibody [EPR17312] (ab200346)
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Recommended applications: ELISA, IHC

Recommended dilution: Recommended dilution:IHC:1:20-1:200

Recommended protocols: check protocols

Name

Anti-SGSH Antibody

Catalogue No.

CSB-PA021200ESR1HU

Reactivity

Human

Immunogen

Recombinant human N-sulphoglucosamine sulphohydrolase protein (273-502AA)

Host

Rabbit

Applications

ELISA, IHC

Recommended dilution

Recommended dilution:IHC:1:20-1:200

Clonality

Polyclonal

Conjugation

unconjugated

Isotype

IgG

Molecular weight

56 kDa

Purification

Antigen Affinity Purified

Storage

Shipped at 4 Celcius Degree. Upon delivery aliquot and store at -20 Celcius Degree or -80 Celcius Degree. Avoid repeated freeze.

Database links

Entrez Gene:6448( Human), Omim:605270( Human), SwissProt:P51688( Human), Unigene:31074( Human)

Protein function

Catalyzes a step in lysosomal heparan sulfate degradation. .

Involvement in disease

Mucopolysaccharidosis 3A (MPS3A) [MIM:252900]: A severe form of mucopolysaccharidosis type 3, an autosomal recessive lysosomal storage disease due to impaired degradation of heparan sulfate. MPS3 is characterized by severe central nervous system degeneration, but only mild somatic disease. Onset of clinical features usually occurs between 2 and 6 years; severe neurologic degeneration occurs in most patients between 6 and 10 years of age, and death occurs typically during the second or third decade of life. MPS3A is characterized by earlier onset, rapid progression of symptoms and shorter survival. . Note=The disease is caused by mutations affecting the gene represented in this entry.

Protein sequence and domain

Belongs to the sulfatase family.

Protein post-translational modifications

The conversion to 3-oxoalanine (also known as C-formylglycine, FGly), of a serine or cysteine residue in prokaryotes and of a cysteine residue in eukaryotes, is critical for catalytic activity. .

Protein cellular localization

Lysosome .

Research area

All research areas>Signaling Intermediates>sulfamidase
(View all antibody categories related to Signaling Intermediates)

Note

AntibodyPlus provides antibody trial sample for your own antibody validation and collects antibody reviews.

Supplier

CUSABIO BIOTECH CO.

Product type

Primary antibody

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