Mouse Monoclonal HPS-1 antibody [5G12G2] (STJ98138)

$379.00

Reactivity: Human
Applications: WB, ELISA
Conjugation: Unconjugated
Supplier: St John’s Laboratory Ltd.

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Mouse Monoclonal HPS-1 antibody [5G12G2] (STJ98138)

Supplier: St John’s Laboratory Ltd.

Recommended applications: WB, ELISA

Recommended dilution: WB 1:500-1:2000; ELISA 1:10000

Recommended protocols: check protocols

Image descriptions:

Click or hover above images to see image description for HPS-1 Monoclonal Antibody.

Alternative names:

Check alternative names for the antibody

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HPS1 antibody, HPS antibody,|Hermansky Pudlak syndrome 1 protein antibody|Hermansky Pudlak syndrome gene antibody|Hermansky Pudlak syndrome type 1 antibody|Hermansky-Pudlak syndrome 1 antibody|Hermansky-Pudlak syndrome 1 protein antibody|HPS antibody|HPS1 antibody|HPS1_HUMAN antibody|MGC5277 antibody|Anti-HPS1 antibody [EP8429(2)] (ab174301)
SCBT cat No: sc-101435|sc-33374|

 

Name

HPS-1 Monoclonal Antibody

Catalogue No.

STJ98138

Reactivity

Human

Specificity

HPS-1 Monoclonal Antibody detects endogenous levels of HPS-1 protein.

Immunogen

Purified recombinant fragment of HPS-1 expressed in E Coli

Host

Mouse

Applications

WB, ELISA

Recommended dilution

WB 1:500-1:2000; ELISA 1:10000

Clonality

Monoclonal

Conjugation

Unconjugated

Isotype

IgG2a

Formulation

HPS-1 Antibody was tube-contained. Ascitic fluid containing 0.03% sodium azide.

Concentration

1 mg/ml

Purification

HPS-1 Antibody was purified using affinity purification.

Storage

-20 Celsius degree. Avoid repeated freeze/thaw cycles.

Alternative antibody names

Hermansky-Pudlak syndrome 1 protein antibody

Database links

Human UniProt/Swiss-Prot:Q92902;Mouse UniPort/Swiss-Prot: O08983;Rat UniProt/Swiss-Port: Q99MK7;Human Entrez Gene: 3257;Mouse Entrez Gene: 192236;Rat Entrez Gene: Rn.17691

Protein names

Hermansky-Pudlak syndrome 1 protein

Protein function

Component of multiple cytoplasmic organelles. Apparently crucial for their normal development and function. May be involved in intracellular protein sorting.

Protein tissue specificity

Ubiquitous.

Involvement in disease

Hermansky-Pudlak syndrome 1 (HPS1) [MIM:203300]: A form of Hermansky-Pudlak syndrome, a genetically heterogeneous autosomal recessive disorder characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS. . Note: The disease is caused by mutations affecting the gene represented in this entry.

Research area

All research areas>Signaling Intermediates>HPS
(View all antibody categories related to Signaling Intermediates)

Note

AntibodyPlus can customize HPS-1 Antibody according to your requirement, including bulk product size,etc. Please contact info@antibodyplus.com. AntibodyPlus provide antibody trial sample for your own antibody validation and collects antibody reviews.

Supplier

St John’s Laboratory Ltd.

Product type

Primary antibody

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