Mouse Monoclonal P504S antibody (STJ98524)

$379.00

Reactivity: Human, Mouse, Rat
Applications: WB, IF
Conjugation: Unconjugated
Supplier: St John’s Laboratory Ltd.

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Mouse Monoclonal P504S antibody (STJ98524)

Supplier: St John’s Laboratory Ltd.

Recommended applications: WB, IF

Recommended dilution: WB 1:1000-1:2000; IF 1:100-1:500

Recommended protocols: check protocols

Image descriptions:

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Alternative names:

Check alternative names for the antibody

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AMACR antibody,|2 methylacyl CoA racemase antibody|2-methylacyl-CoA racemase antibody|Alpha methylacyl CoA racemase antibody|Alpha-methylacyl-CoA racemase antibody|Amacr antibody|AMACR_HUMAN antibody|AMACRD antibody|CBAS4 antibody|EC 5.1.99.4 antibody|Macr1 antibody|RACE antibody|RM antibody|Anti-AMCR antibody (ab175280)
SCBT cat No: sc-136022|sc-81710|sc-514408|sc-514424|

 

Name

P504S Monoclonal Antibody

Catalogue No.

STJ98524

Reactivity

Human, Mouse, Rat

Specificity

P504S Monoclonal Antibody detects endogenous levels of P504S protein.

Immunogen

Purified recombinant human P504S (C-terminus) protein fragments expressed in Ecoli

Host

Mouse

Applications

WB, IF

Recommended dilution

WB 1:1000-1:2000; IF 1:100-1:500

Clonality

Monoclonal

Conjugation

Unconjugated

Formulation

P504S Antibody was tube-contained. Purified in buffer containing 0.1M Tris-Glycine (pH 7.4, 150 mM NaCl) with 0.2% sodium azide, 50% glycerol.

Concentration

1 mg/ml

Purification

P504S Antibody was purified using affinity purification.

Storage

-20 Celsius degree. Avoid repeated freeze/thaw cycles.

Alternative antibody names

Alpha-methylacyl-CoA racemase antibody, 2-methylacyl-CoA racemase antibody

Database links

Human UniProt/Swiss-Prot:Q9UHK6;Mouse UniPort/Swiss-Prot: O09174;Rat UniProt/Swiss-Port: G3V8F9;Human Entrez Gene: 23600;Mouse Entrez Gene: 17117;Rat Entrez Gene: Rn.2590

Protein names

Alpha-methylacyl-CoA racemase , 2-methylacyl-CoA racemase

Protein function

Racemization of 2-methyl-branched fatty acid CoA esters. Responsible for the conversion of pristanoyl-CoA and C27-bile acyl-CoAs to their (S)-stereoisomers. / (2S)-2-methylacyl-CoA = (2R)-2-methylacyl-CoA. / /

Involvement in disease

Alpha-methylacyl-CoA racemase deficiency (AMACRD) [MIM:614307]: A rare autosomal recessive peroxisomal disorder characterized by elevated plasma concentrations of pristanic acid C27-bile-acid intermediates, and adult onset of variable neurodegenerative symptoms affecting the central and peripheral nervous systems. Features may include seizures, visual failure, sensorimotor neuropathy, spasticity, migraine, and white matter hyperintensities on brain imaging. . Note: The disease is caused by mutations affecting the gene represented in this entry.; Congenital bile acid synthesis defect 4 (CBAS4) [MIM:214950]: A disorder characterized by the presence of trihydroxycoprostanic acid in the bile and absence of cholic acid. Patients manifest neonatal jaundice, intrahepatic cholestasis and bile duct deficiency. . Note: The disease is caused by mutations affecting the gene represented in this entry.

Protein sequence and domain

Belongs to the CaiB/BaiF CoA-transferase family.

Protein cellular localization

Peroxisome / Mitochondrion

Research area

All research areas>Signaling Intermediates>P504S
(View all antibody categories related to Signaling Intermediates)

Note

AntibodyPlus can customize P504S Antibody according to your requirement, including bulk product size,etc. Please contact info@antibodyplus.com. AntibodyPlus provide antibody trial sample for your own antibody validation and collects antibody reviews.

Supplier

St John’s Laboratory Ltd.

Product type

Primary antibody

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