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Rabbit Polyclonal Cleaved-Cathepsin A 32k (R326) antibody (STJ90033)
Supplier: St John’s Laboratory Ltd.
Recommended applications: WB, ELISA
Recommended dilution: WB 1:500-1:2000; ELISA 1:10000;
Recommended protocols: check protocols
Click or hover above images to see image description for Cleaved-Cathepsin A 32k (R326) Polyclonal Antibody.
Check alternative names for the antibodyExpand
CTSA antibody, PPGB antibody,|beta galactosidase 2 antibody|BETA GALACTOSIDASE PROTECTIVE PROTEIN antibody|beta-galactosidase 2 antibody|beta-galactosidase protective protein antibody|betagalactosidase 2 antibody|Carboxypeptidase C antibody|Carboxypeptidase L antibody|carboxypeptidase Y-like kininase antibody|Cathepsin A antibody|Ctsa antibody|deamidase antibody|EC 188.8.131.52 antibody|Glactosialidosis antibody|GLB2 antibody|Goldberg Syndrome antibody|GSL antibody|lysosomal carboxypeptidase A antibody|Lysosomal protective protein 20 kDa chain antibody|Lysosomal protective protein antibody|Lysosomal protective protein deficiency antibody|NEURAMINIDASE BETA GALACTOSIDASE EXPRESSION; NGBE antibody|Neuraminidase deficiency with beta-galactosidase deficiency antibody|NGBE antibody|OTTHUMP00000031778 antibody|OTTHUMP00000031781 antibody|PPCA antibody|PPCA deficiency antibody|PPGB antibody|PPGB_HUMAN antibody|Protective protein cathepsin A antibody|Protective protein for beta galactosidase antibody|Protective protein for beta-galactosidase antibody|Protective protein/cathepsin A deficiency antibody|urinary kininase antibody|Anti-Protective protein/Cathepsin A (PPCA) antibody [EPR10435] (ab184553)
SCBT cat No: sc-73766|sc-26049|sc-26050|sc-292167|
Cleaved-Cathepsin A 32k (R326) Polyclonal Antibody
|Catalogue No.|| |
Cleaved-Cathepsin A 32k (R326) Polyclonal Antibody detects endogenous levels of fragment of activated Cathepsin A 32k protein resulting from cleavage adjacent to R326.
Synthesized peptide derived from Cleaved-Cathepsin A 32k (R326) at AA range 250-330
|Recommended dilution|| |
WB 1:500-1:2000; ELISA 1:10000;
|Molecular weight|| |
Cleaved-Cathepsin A 32k (R326) Antibody was tube-contained. Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
Cleaved-Cathepsin A 32k (R326) Antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
-20 Celsius degree. Avoid repeated freeze/thaw cycles.
|Alternative antibody names|| |
Lysosomal protective protein antibody, Carboxypeptidase C antibody, Carboxypeptidase L antibody, Cathepsin A antibody, Protective protein cathepsin A antibody, PPCA antibody, Protective protein for beta-galactosidase antibody
|Protein names|| |
Lysosomal protective protein , Carboxypeptidase C , Carboxypeptidase L , Cathepsin A , Protective protein cathepsin A , PPCA , Protective protein for beta-galactosidase
|Protein function|| |
Protective protein appears to be essential for both the activity of beta-galactosidase and neuraminidase, it associates with these enzymes and exerts a protective function necessary for their stability and activity. This protein is also a carboxypeptidase and can deamidate tachykinins. / Release of a C-terminal amino acid with broad specificity.
|Involvement in disease|| |
Galactosialidosis (GSL) [MIM:256540]: A lysosomal storage disease associated with a combined deficiency of beta-galactosidase and neuraminidase, secondary to a defect in cathepsin A. All patients have clinical manifestations typical of a lysosomal disorder, such as coarse facies, cherry red spots, vertebral changes, foam cells in the bone marrow, and vacuolated lymphocytes. Three phenotypic subtypes are recognized. The early infantile form is associated with fetal hydrops, edema, ascites, visceromegaly, skeletal dysplasia, and early death. The late infantile type is characterized by hepatosplenomegaly, growth retardation, cardiac involvement, and a normal or mildly affected mental state. The juvenile/adult form is characterized by myoclonus, ataxia, angiokeratoma, mental retardation, neurologic deterioration, absence of visceromegaly, and long survival. . Note: The disease is caused by mutations affecting the gene represented in this entry.
|Protein sequence and domain|| |
Belongs to the peptidase S10 family.
|Protein cellular localization|| |
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St John’s Laboratory Ltd.
|Product type|| |
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